World Haemophilia Day 2022, History, Theme, and About Haemophilia Disease

World Haemophilia Day is celebrated on April 17th every year and it is organized by WFH (World Federation of Haemophilia). World Haemophilia Day is celebrated in an effort to provide better care and diagnosis to the people who are not able to get treated.

On World Haemophilia Day, WFH (World Federation of Haemophilia) raises funds for the people who are suffering from Haemophilia and are not capable of getting treatment on their own.

On April 17, 1989, the World Federation of Haemophilia started World Haemophilia Day. The April 17 date was chosen to celebrate World Haemophilia Day in honor of Frank Schnabel's birthday. The World Federation of Hemophilia was also founded by him.
It is believed that Haemophilia was discovered way back in the 10th century when males started to die after minor injuries due to bleeding. In 1803, Dr. John Conrad Otto started a study on people and discovered that Haemophilia is a hereditary disease. He also found that this disease is passed on to males from their mothers. Later in 1937, Haemophilia was further categorized into Haemophilia A and Haemophilia B.

• World Haemophilia Theme 2016: Treatment for All, The Vision of All
• World Haemophilia Theme 2017: Hear their voices
• World Haemophilia Theme 2018: Sharing Knowledge Makes Us Stronger
• World Haemophilia Theme 2020: Get + Involved
• World Haemophilia Theme 2021: Adapting to Change, Sustaining care in a new world
• World Haemophilia Theme 2022: Access for All: Partnership. Policy. Progress. By involving your government and incorporating hereditary bleeding diseases into national policy, you can make a difference.
• WFH’s goal is to increase health care access and equity for Haemophilia and other inherited bleeding disorders by raising awareness and bringing these diseases to the attention of policymakers.

   

Haemophilia, often known as haemophilia, is a hereditary illness that affects the body's capacity to form blood clots, which is required to stop bleeding. This causes people to bleed for longer after an injury, bruising to be easier, and a greater risk of haemorrhaging (bleeding) in the brain and joints.

Those with a moderate case of the disease may only experience symptoms after an accident or while undergoing surgery. Bleeding into a joint can cause long-term pain, seizures, or a loss of consciousness, whereas bleeding into the brain can cause long-term headaches, seizures, or a loss of consciousness.

Haemophilia is divided into two types: haemophilia A, which is caused by a lack of clotting factor VIII, and haemophilia B, which is caused by a lack of clotting factor IX. Haemophilia C, which is caused by low levels of factor XI, and parahaemophilia, which is caused by low levels of factor V, are two more forms. Cancer, immunological illnesses, and pregnancy are all linked to acquired haemophilia.

The following are some of the most common haemophilia symptoms:

• The joints are leaking blood. It commonly affects the knees, elbows, and ankles, causing swelling, pain, and tightness in the joints.
• Blood builds up in the area when it bleeds into the skin (bruising) or muscle and soft tissue (called a hematoma).
• There may be bleeding in the mouth or gums, as well as bleeding after a tooth is lost that is difficult to stop.
• Hemorrhage associated with circumcision.
• Bruising following vaccines or other shots.
• An infant's head is bleeding after a tough delivery.
• Blood in the feces or urine.
• Nosebleeds that are difficult to stop.
• Bleeding into the brain is a serious problem.
• For some persons with severe haemophilia, a simple hit on the head might result in bleeding into the brain. Although this is a rare occurrence, it is amongst the most serious consequences that can arise. Some of the warning signs and symptoms are as follows:
• Long-term, excruciating headache
• vomiting on a regular basis
• Lethargy or sleepiness
• Doubtful perception
• Sudden clumsiness or weakness
• Seizures or convulsions

Hemophilia can cause a variety of complications, including:

• Internal bleeding is severe. Swelling of the limbs can be caused by deep muscular bleeding. The swelling may put pressure on nerves, causing numbness or pain. It could be life-threatening depending on where the bleeding occurs.
• Bleeding from the mouth or nose into the throat or neck. This can make it difficult for a person to breathe.
• Joint deterioration. Internal bleeding can exert strain on the joints, resulting in excruciating discomfort. Internal bleeding, if left untreated, can lead to arthritis or joint degeneration.
• Infection. There's a higher danger of viral infections like hepatitis C if the clotting factors used to treat haemophilia comes from human blood. The danger is limited due to donor screening processes.
• Treatment with clotting factors causes an adverse response.
• The immune system reacts negatively to the clotting agents that are used to treat bleeding in some persons with severe haemophilia. When this happens, the immune system produces proteins that prevent the clotting factors from operating properly, reducing the effectiveness of treatment.

• Hemophilia is frequently identified within the first year of life in severe cases. Mild versions may not show up till adulthood. After experiencing significant bleeding during medical treatment, some people discover they have haemophilia.
• Clotting-factor tests can show a deficit and help evaluate the severity of haemophilia.
• Genetic testing may be used to detect carriers in persons with a family history of haemophilia, allowing them to make educated decisions about becoming pregnant.
• It's also possible to find out if the foetus has haemophilia during pregnancy. However, there are potential hazards to the foetus as a result of the tests. With your doctor, go about the advantages and disadvantages of testing.

• The most common therapy for severe haemophilia is to have the clotting factor replaced through a venous tube.
• This replacement therapy can be used to treat an ongoing bleeding episode. It can also be administered on a regular basis at home to assist reduce bleeding. Continuous replacement therapy is given to some patients.
• Replacement clotting factors can be made from donated blood. Recombinant clotting factors are similar compounds manufactured in a lab rather than from human blood.


• Other options include:


• Fibrin sealants are a type of fibrin sealant. To encourage clotting and healing, they can be applied directly to wound sites. Fibrin sealants are particularly effective in the dental field.
• Fibrin sealants are a type of fibrin sealant. To encourage clotting and healing, they can be applied directly to wound sites. Fibrin sealants are particularly effective in the dental field.
• Minor cuts require immediate attention. The bleeding can usually be controlled with pressure and a bandage. Apply an ice pack to minor spots of bleeding beneath the skin. Ice pops can help to stop minor bleeding in the mouth.
• Desmopressin - This hormone can cause the body to release more clotting factors in some cases of mild haemophilia. It can be injected gently into a vein or sprayed into the nose.
• Emicizumab (Hemlibra) is a kind of antibody. This is a more recent medication that does not contain clotting factors. In persons with haemophilia A, this medication can help avoid bleeding episodes.
  
  Physical therapy is a type of treatment that involves the use of If internal bleeding has injured your joints, it may help to alleviate the signs and symptoms. Surgery may be required if the damage is severe. Medications that keep clots from forming. These drugs, also known as anti-fibrinolytics, assist in preventing blood clots from forming.